Motor function and presence of fatigue symptoms in patients wift muscular dystrophies
DOI:
https://doi.org/10.34024/rnc.2024.v32.15627Keywords:
Muscular dystrophies, fatigue, muscle weakness, motor activityAbstract
Introduction. Muscular dystrophies are hereditary and degenerative neuromuscular diseases characterizing the group of myopathies whose main symptom is progressive muscle weakness and fatigue, causing greater functional disability. Objective. To analyze and correlate motor function and the presence of fatigue symptoms in patients with muscular dystrophy. Method. This is a quantitative and cross-sectional study. The sociodemographic profile of the participants was analyzed, the Severity of Fatigue Scale (FSS) Hand dynamometry, Motor Function Measure (MFM-32) and Medical Research Council (MRC) were used as evaluation instruments. Results. The sample consisted of 66 participants, divided into 3 groups, Duchenne Muscular Dystrophy (DMD), Limb Girdle Muscular Dystrophy (LGMDs) and Steinert Myotonic Dystrophy (DMS), most males 39 (59.1%). Patients with DMD had lower scores on the MFM-32 compared to the others (23.5±12.6). Fatigue was reported in 45 (68.2%) participants, mostly moderately 24 (36.4), with a higher prevalence in individuals with DMS, however, no significant difference was observed between groups. There was no correlation between the analyzed variables. Conclusion. Motor function is impaired mainly in individuals with DMD. Fatigue is present in most participants, with a higher prevalence in those with DMS, but there is no correlation between these two evaluated variables.
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References
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Copyright (c) 2024 Geovane Balçanufo de Souza e Silva, Natália Guimarães Melo, Francine Aguilera Rodrigues da Silva, Graziella França Bernardelli Cipriano, Letícia de Araújo Morais
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Accepted 2024-02-06
Published 2024-02-22
