Síndrome de Guillain-Barré na infância:
relato de caso
DOI:
https://doi.org/10.34024/rnc.2007.v15.8682Palavras-chave:
Síndrome de Guillain-Barré, Polineuropatias, CriançaResumo
A síndrome de Guillain-Barré é uma polineurorradiculopatia inflamatória desmielinizante aguda ou sub-aguda, caracterizada clinicamente por paralisia flácida, arreflexia profunda e dissociação albumino-citológica no líquor. Entre as polineuropatias adquiridas, a SGB é uma afecção que pode ocorrer em crianças, devendo ser lembrada após a instalação aguda ou sub-aguda de paralisia de caráter ascendente, freqüentemente precedida por infecção respiratória ou gastrointestinal. Relatamos o caso de um paciente, 4 anos, sexo masculino, com diagnóstico de Síndrome de Guillain-Barré e comprometimento eletrofisiológico residual do nervo fibular comum bilateralmente.
Downloads
Métricas
Referências
Guillain G, Barré JA, Strohl A. Sur un syndrome de radiculoneurite avec hyperalbuminose du liquide cephalo-rachidien sans reaction cellulaire; remarques sur les caracteres cliniques et graphiques des reflexes tendineux. Bull Soc Med Hop Paris 1916;40:462.
Buompadre MC, Gáñez LA, Miranda M, Arroyo HA. Variantes inusuales del síndrome de Guillain-Barré en la infancia. Rev Neurol 2006;42(2):85-90.
Honavar M, Tharakan KJ, Hughes RAC. A clinicopathological study of the Guillain-Barré syndrome: nine cases and literature review. Brain 1991;114:1245-69.
North K. New perspectives in pediatric neuromuscular disorders. J Child Neurol 1999;14:26-57.
Korinthenberg R, Schessl J, Kirschner J, Mönting JS. Intravenously administered immunoglobulin in the treatment of childhood Guillain-Barré syndrome: A randomized trial. Pediatrics 2005;116:8-14.
Dias-Tosta E, Kückelhaus CS. Guillain-Barré Syndrome in a population less than 15 years old in Brazil. Arq Neuropsiquiatr 2002;60(2-B):367-73.
Aids to the examination of the peripheral nervous system. 4th ed. Edinburgh: WB Saunders, 2000, pp. 1-2.
Monteiro JP, Fonseca S, Proença J, Calhau P, Braga M, Fonseca MJ. Síndrome de Guillain-Barré en edad pediátrica. Experiencia de la Unidad de Neuropediatría de un hospital portugués. Rev Neurol 2006;42(3):144-9.
Santana JCB, Garcia PCR, Einloft PR, Kipper DJ, Chiapin NL, Skrsypcsak F. Distúrbios autonômicos na Síndrome de Guillain-Barré: experiência de 13 anos em UTI pediátrica. J Pediatr 1996;72(1):20-6.
Royden-Jones H. Childhood Guillain-Barré syndrome: clinical presentation, diagnosis and therapy. J Child Neurol 1996;11:4-12.
Ryan MM. Guillain-Barre syndrome in childhood. J Paediatr Child Health 2005;41:237-421.
Evans OB, Vedanarayanan V. Guillain-Barré syndrome. Pediatr Rev 1997;18:10-6.
Sladky JT. Guillain-Barre syndrome in children. J Child Neurol 2004;19(3):191-200.
Cohn CA, Zagelbaun GC. Clinical manifestation of inspiratory muscle fatigue. Am J Med 1983;73(6):308-15.
Nguyen DK, Agenarioti-Bélanger S, Vanasse M. Pain and the Guillain-Barré syndrome in children under 6 years old. J Pediatr 1999;134:773-6.
Ortiz-Corredor F. Factores que influyen en el pronóstico del síndrome de Guillain-Barré infantil. Rev Neurol 2004; 38:518-23.
Ropper AH. Current concepts: the Guillain-Barré Syndrome. N Engl J Med 1992;326:1130-6.
Willians PL. Gray’s Anatomy. 38th ed. Edinburgh: Churchill Livingstone, 1999, 1634 p.
Schessl J, Funakoshi K, Susuki K, Gold R, Korinthenberg R. Anti-GT1a IgG antibodies in a child with severe Guillain-Barré syndrome. Pediatr Neurol;35(4):277-9.
Takayanagui OM, Menezes RF, Barbosa JE, Jardim E. Líquido cefalorraquiano (LCR) na síndrome de Guillain-Barré: análise de 62 casos. Rev Bras Neurol 1993;29(5):152-5.
Nagasawa K, Kuwabara S, Misawa S, Fujii K, Tanabe Y, Yuki N, et al. Electrophysiological subtypes and prognosis of childhood Guillain-Barré syndrome in Japan. Muscle Nerve 2006;33(6):766-70.
Hung PL, Chang WN, Huang LT, Huang SC, Chang YC, Chang CJ, et al. A clinical and electrophysiologic survey of childhood Guillain-Barré syndrome. Pediatr Neurol 2004;30(2):86-91.
Nascimento OJM, Freitas MRG, Escada TM, Araújo E, Araújo APQC, Araújo AQC. Síndrome de Guillain-Barré na criança: tra-tamento com altas doses de imunoglobulina endovenosa. J Pediatr 1992;68:352-6.
Raphael JC, Chastang C, Gadjos P. Intravenous immune globulin versus plasma exchange in Guillain-Barré syndrome. N Engl J Med 1992;327:816-7.
Hughes RAC. Ineffectiveness of high-dose intravenous methylprednisolone in Guillain-Barré syndrome. Lancet 1991;338:1142.
Hughes RAC, Swan AV, van Koningsveld R, van Doorn PA. Corticosteroids for Guillain-Barré syndrome (Cochrane Review). In: The Cochrane Library, Issue 2. Oxford: Update Software, 2006.
Hughes RAC, van der Meché FGA. Corticosteroids for Guillain-Barré syndrome (Cochrane Review). In: The Cochrane Library, Issue 1. Oxford: Update Software, 2006.
Newswanger DL, Warren CR. Guillain-Barré Syndrome. Am Fam Physician 2004;69:2405-10.
Hughes RAC, Wijdicks EF, Benson E, Cornblath DR, Hahn AF, Meythaler JM, et al. Supportive care for patients with Guillain-Barré syndrome. Arch Neurol 2005;62:1194-8.
Downloads
Publicado
Como Citar
Edição
Seção
Publicado: 2007-12-31