Noninvasive Ventilation and Respiratory Physical Therapy for Amyotrophic Lateral Sclerosis patients
DOI:
https://doi.org/10.34024/rnc.2009.v17.8555Keywords:
Amyotrophic Lateral Sclerosis, Ventilation, Physical TherapyAbstract
The Amyotrophic Lateral Sclerosis (ALS) is a neurodegenerative illness, progressive and lethal that generally leads to the death five years after the beginning of the first symptoms. Of this form, the palliative care must begin soon after the confirmation of the clinical diagnosis. At present, the only medication approved for the treatment of the illness, the Riluzole, seems to contribute for the prolongation of the survival of the patients in a period of two the three months. All of the skeletal muscles are affected on the illness progresses, including the respiratory muscles. Objective. To guide the health professionals about the utilization of the Noninvasive Ventilation (NIV) and respiratory physiotherapy in patients with ALS, as well as its indication. Method. Update of articles about NIV and of the respiratory physiotherapy in patients with ALS, in the last years in the data bases Medline, SciELO, Cochrane and Lilacs. Conclusion. The NIV can prolong the survival and improve the quality of life of the patients with ALS during the course of the illness. Moreover, the management of the respiratory muscles, when applied in a care way, improves the pulmonary function, minimizes the decline of the current volume and delays the beginning of the respiratory insufficiency.
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