Síndrome do Homem do Barril como forma atípica de Esclerose Lateral Amiotrófica

Autores

  • Marco Orsini Undergraduate in Medicine, Associate Professor of Neurologic Rehabilitation and Scientific Initiation, Escola Superior de Ensino Helena Antipoff (ESEHA), Department of Neurology, Federal Fluminense University – UFF, Niterói, RJ.
  • Marcos RG de Freitas MD, PhD, Chair of Neurology and Head of Staff, Department of Neurology, UFF, Niterói, RJ
  • Mariana P Mello Physical Therapist, Program of Scientific Initiation, Neurology Department, UFF, Niterói, RJ.
  • Osvaldo JM Nascimento MD, PhD, Chair of Neurology, Department of Neurology, UFF, Niterói, RJ
  • Carlos Henrique Melo Reis Chair of Neurology, Department of Neurology, Valença University of Medicine, Valença, RJ.

DOI:

https://doi.org/10.34024/rnc.2009.v17.8538

Palavras-chave:

Esclerose Amiotrófica Lateral, Doenças Neuromusculares, Células do Corno Anterior, Doença dos Neurônios Motores

Resumo

A síndrome do “Homem do Barril” faz referência a um quadro de fraqueza muscular braquial bilateral, a qual incapacita os pacientes em atividades funcionais com a elevação dos membros superiores. Desde sua descrição, existem alguns casos de pacientes com tal síndrome, de etiologias variadas. Realizamos a leitura do artigo de Sasaki et al. “Atypical form of amyotrophic lateral sclerosis: a new term to define a previously well-known form of ALS” (2000), a respeito de uma distribuição atípica da Esclerose Lateral Amiotrófica (ELA). O quadro de atrofia muscular nesses pacientes difere da típica ELA, devido ao envolvimento confinado nos membros superiores, predominantemente no terço proximal e cintura escapular.

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2009-12-31

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1.
Orsini M, Freitas MR de, Mello MP, Nascimento OJ, Reis CHM. Síndrome do Homem do Barril como forma atípica de Esclerose Lateral Amiotrófica. Rev Neurocienc [Internet]. 31º de dezembro de 2009 [citado 23º de junho de 2025];17(4):401-3. Disponível em: https://periodicos.unifesp.br/index.php/neurociencias/article/view/8538