Frequência de escoliose em miopatias: revisão de escopo
DOI:
https://doi.org/10.34024/rnc.2024.v32.16464Palavras-chave:
Escoliose, Miopatias, Miopatias CongênitasResumo
Introdução. A escoliose é caracterizada como um desvio lateral na coluna vertebral, que pode ser acompanhado de componente rotacional, resultando em uma curvatura com angulação variável, conforme medida pelo ângulo de Cobb. Escoliose é um achado descrito em doenças neuromusculares que levam a comprometimento de musculatura paravertebral, que deve ser monitorada para detecção e intervenção precoces. Assim, o objetivo desta revisão de literatura é investigar a ocorrência e frequência de escoliose nas várias miopatias, para aumentar o grau de suspeição clínica e intervenção no momento adequado. Método. As buscas foram realizadas no banco de dados da PubMed, para artigos publicados entre 1965-2023, com as palavras-chave “myopathy” e “scoliosis”. 112 dos 229 artigos originais encontrados atenderam aos critérios de inclusão e todos os artigos selecionados foram avaliados criticamente por dois avaliadores independentes. As seguintes variáveis foram selecionadas desses artigos: autor, ano, tipo de miopatia, mutação associada, idade, sexo, severidade da escoliose e intervenção. Resultados. As miopatias associadas à escoliose nessa revisão foram, em ordem de frequência, as distrofias musculares congênitas (14-100%), as distrofias musculares progressivas como a forma de Duchenne (100%) e as miopatias congênitas (5-100%). A quantificação da intensidade da escoliose teve predominância de casos severos, seguido de casos leves. Em relação às intervenções, foram relatadas a fisioterapia e a intervenção cirúrgica, na maioria dos casos. Conclusão. Escoliose é um achado frequente em miopatias, porém com poucos dados prospectivos da intensidade e do impacto das intervenções em grande parte delas. Mais estudo são necessários nessa área.
Métricas
Referências
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Copyright (c) 2024 Andréa Oliver Gomes, Larissa Fany Cristina de Marci Souza Lima, Marcelo Wajchenberg, Acary Souza Bulle Oliveira, Helga Cristina Almeida da Silva
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Aprovado 2024-10-17
Publicado 2024-11-08
