Síndrome da Cabeça Caída na Esclerose Lateral Amiotrófica:
Relato de Caso
DOI:
https://doi.org/10.34024/rnc.2008.v16.8624Palavras-chave:
Esclerose Amiotrófica Lateral, Doenças Neuromusculares, EletromiografiaResumo
A síndrome da cabeça caída (SCC) é uma condição relativamente rara decorrente de um quadro de fraqueza nos músculos extensores do pescoço, sendo encontrada em diversas doenças neuromusculares, como a esclerose lateral amiotrófica (ELA). Relatamos o caso de uma paciente com ELA que evoluiu para SCC após aproximadamente 4 anos de doença. O exame de eletroneuromiografia mostrou desnervação ativa e crônica da musculatura bulbar e dos segmentos cervicais, torácicos e lombo-sacros. O uso de colar cervical para estabilização da coluna foi eficaz neste caso. Apesar da SCC não ser uma situação relativamente freqüente na ELA, ressaltamos a necessidade de investigação do diagnostico de ELA em pacientes com SCC.
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