Síndrome do Homem do Barril
histórico e etiologias várias
DOI:
https://doi.org/10.34024/rnc.2009.v17.8573Palavras-chave:
Doenças Neuromusculares, Doença do Neurônio Motor, Corno AnteriorResumo
A síndrome do “homem do barril” (SHB) faz referência a um quadro de fraqueza muscular braquial bilateral, de predominio proximal, que impossibilita os pacientes na execução de atividades funcionais relacionadas com a elevação dos membros superiores. Desde sua descrição, inúmeros casos de pacientes com essa síndrome foram relatados, cuja etiopatogenia difere daquela descrita inicialmente. As mais frequentes causas de SHB são distúrbios vasculares cerebrais, cirurgias cardíacas e extracardíaca com demonstração de hipotenção arterial, metásteses cerebrais, e o envolvimento da ponte e medula espinhal. Paralisia braquial bilateral também ocasiona quadro similar. Assim, o substrato fisiopatológico que se relaciona a SHB, em alguns casos, é incerto e merece atenção.
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