Síndrome do Homem do Barril como forma atípica de Esclerose Lateral Amiotrófica

Autores

  • Marco Orsini Undergraduate in Medicine, Associate Professor of Neurologic Rehabilitation and Scientific Initiation, Escola Superior de Ensino Helena Antipoff (ESEHA), Department of Neurology, Federal Fluminense University – UFF, Niterói, RJ.
  • Marcos RG de Freitas MD, PhD, Chair of Neurology and Head of Staff, Department of Neurology, UFF, Niterói, RJ
  • Mariana P Mello Physical Therapist, Program of Scientific Initiation, Neurology Department, UFF, Niterói, RJ.
  • Osvaldo JM Nascimento MD, PhD, Chair of Neurology, Department of Neurology, UFF, Niterói, RJ
  • Carlos Henrique Melo Reis Chair of Neurology, Department of Neurology, Valença University of Medicine, Valença, RJ.

DOI:

https://doi.org/10.34024/rnc.2009.v17.8538

Palavras-chave:

Esclerose Amiotrófica Lateral, Doenças Neuromusculares, Células do Corno Anterior, Doença dos Neurônios Motores

Resumo

A síndrome do “Homem do Barril” faz referência a um quadro de fraqueza muscular braquial bilateral, a qual incapacita os pacientes em atividades funcionais com a elevação dos membros superiores. Desde sua descrição, existem alguns casos de pacientes com tal síndrome, de etiologias variadas. Realizamos a leitura do artigo de Sasaki et al. “Atypical form of amyotrophic lateral sclerosis: a new term to define a previously well-known form of ALS” (2000), a respeito de uma distribuição atípica da Esclerose Lateral Amiotrófica (ELA). O quadro de atrofia muscular nesses pacientes difere da típica ELA, devido ao envolvimento confinado nos membros superiores, predominantemente no terço proximal e cintura escapular.

Referências

Sasaki S, Gamez J, Cervera C, Codina A. Atypical form of amyotrophic lateral sclerosis: a new term to define a previously well known form of ALS. J Neurol Neurosurg Psychiatr 2000;68:118-9. DOI: https://doi.org/10.1136/jnnp.68.1.118b

Sasaki S, Makoto I. Atypical form of amyotrophic lateral sclerosis. J Neurol Neurosurg Psychiatr 1999;66:581-5. DOI: https://doi.org/10.1136/jnnp.66.5.581

Wahl CC. “Man-in-the-Barrel” Syndrome After Endoscopic Sinus Surgery. Anesth Analg 1998;87:1196-8.

Sage JI. “Man in the barrel” syndrome after cerebral hypoperfusion: clinical description, incidence, and prognosis. Ann Neurol 1983;14:131.

Crisostomo EA, Suslavich FJ. Man-in-the-barrel syndrome associated with closed head injury. J Neuroimaging 1994;4:116-7. DOI: https://doi.org/10.1111/jon199442116

Alberca R, Iriarte LM, Rasero P, Villalobos F. Brachial diplegia in central pontine myelinolysis. J Neurol 1985;231: 345-6. DOI: https://doi.org/10.1007/BF00313715

Dide M, Lhermite J. La diplegie brachiale spasmodique consecutive aux blessures par coups de feu de la region cervicale. Progres Med 1917;1:1-3.

Katz JS, Wolfe GI, Andersson PB, Saperstein DS, Elliott JL, Nations SP, et al. Brachial amyotrophic diplegia: a slowly progressive motor neuron disorder. Neurology 1999;53:1071-6. DOI: https://doi.org/10.1212/WNL.53.5.1071

Bell HS. Paralysis of both arms from injury of the upper portion of the pyramidal decussation: ‘cruciate paralysis’. J Neurosurg 1970;33:376-80. DOI: https://doi.org/10.3171/jns.1970.33.4.0376

Mohr JP. Distal field infarction. Neurology 1969;12:279.

Sage JI, Van-Uitert RL. Man-in-the-barrel syndrome. Neurology 1986;36:1102-3. DOI: https://doi.org/10.1212/WNL.36.8.1102

Clerget L, Lenfant F, Roy H, Giroud M, Salem DB, Freysz M. Man-in-the-Barrel Syndrome after Hemorrhagic Shock. J Trauma 2003;54:183-6. DOI: https://doi.org/10.1097/00005373-200301000-00024

Hurley JP, Wood AE. Isolated man-in-the-barrel syndrome following cardiac surgery. Thorac Cardiovasc Surg 1993;41:252-4. DOI: https://doi.org/10.1055/s-2007-1013865

Deleu D, Salim K, Mesraoua B, Siddig AE, Hail HA, Hanssens Y. ‘‘Man-in-the-barrel’’ syndrome as delayed manifestation of extrapontine and central pontine myelinolysis: Beneficial effect of intravenous immunoglobulin. J Neurol Sci 2005;237:103-6. DOI: https://doi.org/10.1016/j.jns.2005.05.012

Berg D, Müllges W, Koltzenburg M, Bendszus M, Reiners K. Manin-the-barrel syndrome caused by cervical spinal cord infarction. Acta Neurol Scand 1998;97:417-9. DOI: https://doi.org/10.1111/j.1600-0404.1998.tb05977.x

Luengo-Álvarez J, Ramírez-Moreno JM, Falcón-García A, Casado-Narajo I. Neuralgia amiotrófica bilateral y simétrica que simula el síndrome del ‘hombre en el barril’. Rev Neurol 2006;43:123-4. DOI: https://doi.org/10.33588/rn.4302.2005748

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2009-12-31

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1.
Orsini M, Freitas MR de, Mello MP, Nascimento OJ, Reis CHM. Síndrome do Homem do Barril como forma atípica de Esclerose Lateral Amiotrófica. Rev Neurocienc [Internet]. 31º de dezembro de 2009 [citado 5º de outubro de 2026];17(4):401-3. Disponível em: https://periodicos.unifesp.br/neurociencias/article/view/8538