Miosite por Corpos de Inclusão Familiar (MCIF)

Atualização

Autores

  • Marco Orsini Physical therapist, Associate Professor of Neurologic Rehabilitation, Escola Superior de Ensino Helena Antipoff (ESEHA), Voluntary Assistant of the Department of Neurology, Universidade Federal Fluminense – UFF, Niterói-RJ, Brazil.
  • Mariana Pimentel Mello Physical Therapist and Student of the Program of Scientific Initiation, Neurology Department, UFF, Niterói-RJ, Brazil.
  • Marcos RG de Freitas Neurologist, Head of Staff, Department of Neurology, UFF, Niterói-RJ, Brazil.
  • Osvaldo JM Nascimento Neurologist, UFF, Niterói-RJ, Brazil.

DOI:

https://doi.org/10.34024/rnc.2009.v17.8579

Palavras-chave:

Miosite, Corpos de Inclusão, Doenças Neuromusculares

Resumo

Miosite por corpos de inclusão familiar é uma doença extremamente rara, caracterizada por início tardio, seletivo e com precoce envolvimento dos músculos quadríceps, flexores dos dedos e do antebraço, e ligeiro aumento nos níveis séricos de creatina cinase (CK). Histologicamente as fibras musculares apresentam vacúolos marginados e infiltrados inflamatórios. A combinação de achados clínicos, imunopatológicos, histológicos e imunogênicos indicam que esses pacientes apresentam uma doença de características similares a miosite por corpos de inclusão esporádica.

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Referências

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Publicado

2009-06-30

Como Citar

Orsini, M., Mello, M. P., Freitas, M. R. de, & Nascimento, O. J. (2009). Miosite por Corpos de Inclusão Familiar (MCIF): Atualização. Revista Neurociências, 17(2), 193–195. https://doi.org/10.34024/rnc.2009.v17.8579

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Seção

Atualização
Recebido: 2019-02-08
Publicado: 2009-06-30

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